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Companion Case for Case #2

February 9, 2017 11:10 pm / Leave a Comment / kirschj

2 year old female with microcephaly and developmental delay referred to MRI for evaluation of valvular pulmonary stenosis and dilatation of the MPA and Aorta.

Presumed pulmonary valve blood cyst on MRI. On MRI the mass is hypointense on SSFP, isointense on T1 and doesn’t suppress with Fat Sat, and hyperintense on T2. It is not perfused on first pass perfusion imaging, and the rim shows enhancement similar to valve tissue on LGE imaging.

Echo shows cyst attached to pulmonary valve tissue. The tumor was first noticed on the MR and in retrospect had been present on the echo.

 

Courtesy: JC Muñiz

Posted in: Case

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